Abstract:

Sickle cell disease is considered as a major complication and risk factor for perinatal morbidity /mortality. Literature document that most pregnancies complicated by sickle cell are likely to result in live birth, but the consequences of influence of the disease for the pregnancy/newborn remains a significant concern for health care providers worldwide. According to the bibliography obstetrical-fetal risks are due to the metabolic demands, hypercoagulable state, and vascular stasis associated with pregnancy characterized normally for blood cells to be able to carry oxygen to the growing fetus. With sickle cell anemia, the abnormal red blood cells and anaemic characteristics of the disease physiopathology may result in lower amounts of oxygen going to the developing baby with negative outcome for the future newborn.

Research review studies agreed that access of the pregnant client to a multidisciplinary care team knowledgeable about sickle cell disease and high-risk obstetrics can significantly decrease feto-maternal morbidity and mortality. Example: decreases in spontaneous miscarriage, in perinatal death rates and lowered incidence of preterm labour. Active prenatal management include: education; genetic counselling and prenatal diagnosis for couples at risk; improving nutritional status; vaccination for disease prevention, and early detection of bacterial infection.

Objective of this study was to explore active nursing management of the pregnant women with sickle cell disease, including education, treatment and nursing intervention.

Method: use of English Literature review current through: Jun 2017, Data were searched using MEDLINE, EMBASE, PUBMED and COCHRANE Systematic Reviews.

Keywords: Sickle Cell Disease, complication, feto-maternal risk, active nursing management.

References:

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